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Melanotic neuroectodermal tumor of infancy
Case Detail
| Anatomy: Genitourinary |
 Joseph Junewick, MD FACR |
| Diagnostic Category: Neoplasia Benign |
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| Created: over 3 years ago |
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| Updated: over 2 years ago |
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| Tags:
PEDS
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| Modality/Study Types:
US
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Activities:  PDF  ImageJA |
History
Nearly 5 month old male with scrotal mass.
Case Images
Diagnosis
Epididymal melanotic neuroectodermal tumor of infancy
Clinical Notes
Elevated vanillylmandelic acid (VMA).
Findings
US – Hydrocele with hypervascular mass adjacent to the normal testicle.
Gross Pathology – The tumor originates from the epididymus. The cut surface of the tumor is white and fibrous with a punctate central dark spot.
Discussion
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare tumor. More than 90% involve the head and heck (most often the maxilla) but skin, mediastinum, long bones, uterus, ovary and epididymus have been reported. MNTI are almost always solitary with an average age of onset between 1 and 6 months. While MNTI grow very rapidly, the clinical course is benign with only 15% incidence of local recurrence.
Reference
Lee SB et al. Melanotic Neuroectodermal Tumor of Infancy in the Epididymus: A Case Report. Kor J Ped (2004); 47(12):1334-7.