Splenic Hemangioendothelioma
Case Detail
| Anatomy: Gastrointestinal |
Joseph Junewick, MD FACR |
| Diagnostic Category: Neoplasia Benign |
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| Created: over 3 years ago |
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| Updated: over 2 years ago |
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| Tags:
PEDS
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| Modality/Study Types:
US
MR
CT
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Activities: PDF ImageJA |
History
9 month old female with left upper quadrant mass on well child examination.
Case Images
Diagnosis
Splenic hemangioendothelioma (SH)
Clinical Notes
Hemoglobin – 7.6 (low)
Platelet – 436K (high)
WBC – 23.7K (high)
human chorionic gonadotropin – <1 (normal)
alpha feto-protein – 11.5 (normal)
Findings
US – Large hypervascular exophytic splenic mass, slightly hypoechoic to the spleen.
CT – Confirms slightly heterogeneous isodense splenic origin mass.
MRI – Mass is hypointense to spleen on T2 and hyperenhancing on post-gadolinium images.
Discussion
SH is a very rare tumor with low malignant potential previously thought to represent angiosarcoma. Patients are often young adults with no gender predilection who present with a palpable mass and hypersplenism. Diagnosis is unlikely to be made by imaging alone.



